Abstracto

Intraosseous synovial sarcoma of the body of the scapula

Pedro Cardoso, Andre Coelho, Joao Esteve and Ricardo Rodrigues-Pinto

Background: Intraosseous Synovial Sarcoma is extremely rare. To the author’s knowledge this is the first description of an intraosseous synovial sarcoma of the scapula.
Case description: Here, a case of a giant Synovial Sarcoma of the body of the scapula is reported. Diagnosis was based on histologic (haematoxylin and eosin) pattern and immunohistochemical analysis and confirmed by cytogenetics. The patient underwent a Malawer type IV resection. Four years after index surgery the disease recurred and another resection was performed followed by radiotherapy. Seven years after initial presentation this patient is disease-free.
Literature review: To date, only 10 cases of intraosseous synovial sarcoma have been reported, being located to the mandible, elbow, proximal femur, tibia and sacrum. In all cases, wide surgical resection was advocated but, despite optimal treatment, prognosis remained poor.
Clinical relevance: In this study a novel localization for intraosseous synovial sarcoma is described and its engagement with wide surgical resection (Tikhoff-Linberg procedure - total extra-articular scapulectomy) is presented. Prompt surgical and adjuvant treatment led a favorable prognosis.